摘要
目的:分析锁骨颅骨发育不良综合征(CCD)患者的颅面部特征,为临床早期诊断提供参考。方法:收集8例CCD患者的临床资料,依据正畸临床常规拍摄的面像、头颅定位侧位片、全口曲面断层片分别分析患者的面部特征、颈椎骨龄、以及颌面骨骼特征。结果:4例患者处于生长发育高峰前期或高峰期,4例患者的生长发育基本完成。所有患者面部特征表现:前额部隆起、眼裂倾斜;面中发育不足、面下高度比例不调仅在生长发育完成的患者中明显表现。颌面骨骼特征分析显示:所有患者的喙突指向上方/后上方,下颌升支前后缘接近平行,下颌角不同程度缺失;额骨隆起,枕骨出现沃姆氏骨,颅底蝶鞍部后凸。结论:CCD患者具有特殊的面容,鼻部、眼部、额部等部位的异常在面中发育不足的特征明显出现前已有所表现,这有助于CCD患者的早期诊断。
Objective：To investigate the craniofacial features in patients with cleidocranial dysplasia （CCD）.Methods：The facial features,cervical vertebral bone age and skeletal abnormalities of 8 patients with CCD were studied by analyzing facial photos,cephalo-metric and panoramic radiographs.Results：4 patients were in the early growth stage and the other 4 in the late period of development. The bossing forehead and inclined eye fissure were observed in all patients,but underdevelopment of midfaces were not obviously pres-ented in younger patients.Morphological abnormalities of craniofacial bones,such as ascending ramus,coronoid process,nasal bones and disappearence of gonial angle were observed in all patients.Conclusion：Some craniofacial malformations in patients with CCD may be presented earlier than underdeveloped midface,which can be helpful for early diagnosis of CCD.
出处
《实用口腔医学杂志》
CAS
CSCD
北大核心
2015年第3期407-411,共5页
Journal of Practical Stomatology
