摘要
儿童肝豆状核变性(hepatolenticular degeneration,HLD)以肝功能衰竭合并溶血性贫血发病的临床表现不典型,需通过各项检查综合判断.肝豆状核变性进展快,预后差,需积极联系肝移植.本文对13例以肝功能衰竭合并溶血性贫血发病的肝豆状核变性儿童患者的临床特点进行分析.
Hepatolenticular degeneration (HLD) in children expressed as liver failure complicated with hemolytic anemia is often atypical in clinical manifestations. The etiological diagnosis of HLD requires comprehensive judgment of various examinations. However, the disease progresses rapidly and the prognosis is poor. Liver transplantation should be considered actively. Clinical characteristics of 13 children with hepatolenticular degeneration expressed as liver failure complicated with hemolytic anemia were analyzed in this article.
作者
王丽旻
张敏
董漪
甘雨
陈大为
王福川
闫建国
朱世殊
WANG Li-min;ZHANG Min;DONG Yi;GAN Yu;CHEN Da-wei;WANG Fu-chuan;YAN Jian-guo;ZHUShi-shu(Pediatric Liver Diseases Therapy and Research Center, Fifth Medical Center of PLA General Hospital, Beijing 100039, China)
出处
《中国肝脏病杂志（电子版）》
CAS
2019年第2期85-88,共4页
Chinese Journal of Liver Diseases：Electronic Version
基金
首都临床特色应用研究(Z181100001718030)
关键词
儿童
肝豆状核变性
肝功能衰竭
溶血
临床特征
预后
Children
Hepatolenticular degeneration
Liver failure
Hemolysis
Clinical characteristics
Prognosis
