摘要
目的 探讨外周性原始神经外胚层肿瘤 (pPNETs)的CT特征 ,提高对本病的认识水平。方法 回顾分析 6例经病理证实的pPNETsCT表现。结果 5例发生在骨骼的pPNETs,CT表现为溶骨性骨质破坏和明显的软组织肿块。骨质破坏区无骨膜增生、骨质硬化和瘤骨形成 ;软组织肿块的密度可均匀或不均匀。 1例放疗后软组织肿块有明显缩小。 1例发生在右胸腔的pPNETs(Askin瘤 ) ,CT表现为巨大软组织肿块 ,侵犯纵隔 ,密度不均匀 ,有中度不均匀强化 ,周围骨骼无破坏。手术切除后 4个月 ,在右胸壁再发密度均匀的小肿块 ,有中度均匀强化。结论 pPNETs的CT表现缺乏特征性 ,但能较好地显示肿瘤的内部结构、明确肿瘤的范围 ,有助于本病的鉴别诊断、判断手术可切除性、检出远处转移和评价治疗效果。
Objective To study the CT features and enhance the knowledge of peripheral primitive neuroectodermal tumors(pPNETs). Methods The CT appearances of 6 patients with pPNETs pathologically proved were analyzed retrospectively. Results The CT findings of 5 bone pPNETs were soft mass of homogeneous or heterogeneous density and osteolytic destruction without osteosclerosis, periosteum reaction and tumor bone formation. Follow up CT showed the mass shrunken significantly after radiotherapy in one case. In 1 patient of chest Askin tumor, the lesion appeared as a vast heterogeneous soft mass with moderate inhomogeneous enhancement. The mass invaded mediastinum and local bone destruction were not detected. Four months after operation, a small homogeneous tumor occurred in right chest wall with moderate homogeneous enhancement. Conclusion The manifestations of pPNETs on CT have no characteristics. However, CT can show the intra tumor structures and the extent of the tumor very well, which is helpful in differentiating diagnosis,predicting resectability, detecting distant metastases and evaluating the response to treatment.
出处
《中华放射学杂志》
CAS
CSCD
北大核心
2001年第7期535-537,共3页
Chinese Journal of Radiology
关键词
骨肿瘤
外周神经外胚瘤
CT
诊断
Bone neoplasms
Neuroectodermal tumor,peripheral
Tomography, X ray computed
