马凡氏综合征诊疗进展(附1例合并升主动脉与腹主动脉夹层动脉瘤病例报告)
被引量：2
摘要
马凡氏综合征(Marfan's Syndrome)是主要累及心血管、骨骼与眼的常染色体显性遗传性疾病。心血管疾病为致命性病变。随着对该病认识的深入及诊治手段的改进,预后较前有明显改善。现将所遇到的一例典型马凡氏综合征合并升主动脉与腹主动脉夹层动脉瘤病例报告如下。
同被引文献30
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