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血友病的治疗进展 被引量:5

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摘要 血友病是一组X连锁隐形遗传性出血性疾病,主要表现为自发性出血或外伤、手术后出血,反复关节肌肉出血可以致残,危险部位出血甚至威胁生命。替代治疗是血友病唯一有效的治疗方法,同时需要康复、理疗、护理、心理关怀等综合治疗。治疗理念已从出血后按需治疗发展为预防治疗,未来的发展方向将是基因检测阻断患者出生,长效凝血因子的输注以及基因治疗等,从而使患者彻底摆脱疾病的困扰。
作者 周敏 徐鸣
出处 《华西医学》 CAS 2012年第2期206-209,共4页 West China Medical Journal
关键词 血友病 治疗
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参考文献29

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共引文献83

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