摘要
目的:探讨儿童中耳先天性胆脂瘤的临床症状、位置、影像学特征、治疗及预后。方法:回顾性分析9例中耳先天性胆脂瘤患儿的临床资料。结果:患儿均行手术治疗,5例有听小骨破坏,术后复发4例,复发率为44.4%。平均随访7.4年,术前平均听阈为28 dB,术后平均听阈为26 dB。结论:中耳先天性胆脂瘤临床少见,发病隐匿,单侧传导性聋为主要表现。术前诊断可根据Levenson诊断标准和CT检查结果。其预后和复发率与病变范围、手术方式、是否2次手术有关。
Objective：To investigate the location,clinical symptom,image features,treatment and prognosis of the congenital middle ear cholesteatoma.Method：Retrospective review of 9 patients treated at Department of otolaryngology Head and neck Surgery,the affiliated Hospital of the first Strasbourg University,France.Result：The mean age was 6.1 years.Including 7 boys and 2 girls with hearing loss,and 7 of them suffered conductive hearing loss.Typical cholesteatomas were found behind posterior tympanic membrane according the otoscopic examinations in 6 cases.CT were completed in 8 of 9 cases,spheroid or ovoid masses were found in the tympanic cavities,most of them located in the posterior region.All of the patients underwent the surgical treatment,5 of 9 cases had the ossicular erosion.Four of 9 cases had the residual diseases.All of the cases were followed-up at the mean period of 5.3 years,the preoperative hearing threshold is 28 dB compared with 26dB of postoperative hearing threshold.Conclusion：Congenital middle ear cholesteatoma is a rare and hiding lesion.The symptoms are more typical in childern than that in adults,which is unilateral conductive hearing loss.Likewise,the preoperative CT scanning is important.The rate of residual lesions and prognosis of congenital cholesteatoma is mainly depended on the extension and the methods of the surgery,revision surgery as well.
出处
《临床耳鼻咽喉头颈外科杂志》
CAS
CSCD
北大核心
2010年第13期601-603,共3页
Journal of Clinical Otorhinolaryngology Head And Neck Surgery
关键词
中耳先天性胆脂瘤
诊断
预后
congenital middle ear cholesteatoma
diagnostic
prognosis
