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性连锁淋巴组织增殖病 被引量:1

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摘要 本病自首次报道迄今已有十多年,受累家族与患儿日益增多,故逐渐受到儿科尤其是免疫工作者的重视。凭借患儿的男性性别,阳性的家族历史,典型的临床症状和 EB 病毒感染的证据,做出诊断并不困难。必要时可借助 EB 病毒 DNA 探针 DXS42、DXS37和 DXS12及兼做噬菌体φX174激发试验最后确诊。本病无特效疗法,可试用抑制 EB 病毒的抗生素、干扰素、白细胞介素以及免疫球蛋白。
作者 龚新顺
出处 《国外医学(儿科学分册)》 北大核心 1992年第2期60-63,共4页 Foreign Medical Sciences(Section of Pediatrics)
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  • 2Woda BA.Reactive histiocytic disorders. American Journal of Clinical Pathology . 1993
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  • 8Henter JI,Elinder G.Celebromeningeal hemohagocytic lymphohistiocytosis. Seminars in Oncology . 1991
  • 9Malone M.The histiocytoses of childhoed. Histopathology . 1991
  • 10Henter J I,Elinder G,ost A,et al.Diagnostic guidelines for hemophagocytic lymphohistiocy tosis. Seminars in Oncology . 1991

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