摘要
目的 :提高对Mondini畸形的认识。方法 :收集从 1995年 2月～ 2 0 0 1年 11月确诊的Mondini畸形的 4 8例临床资料 ,对该病的临床特征、影像学表现等进行分析。结果 :重度耳聋、说话延迟、行走不稳是Mondini畸形的重要特征。结论 :CT与MRI检查是确诊的主要依据。避免致畸因素的影响是预防本病发生的重要措施。助听器是目前主要的治疗手段 。
Objective:To improve the ability to diagnosis the Mondini dysplasis, 48 cases of Mondini dysplasis were reported.Method:The clinical data of 48 cases were collected. The clinical manifestation and the examination of CT and MRI and treatment of the Mondini dysplasis were discussed.Result:Most of them were deaf when they were babies. The prolonged speaking and unsteading were important clinical feature.Conclusion:The diagnosis of the disease is based on the examination of the hight resolution tomography and magenatic resonance image of the temporal bone. Hearing aid is common management to the disease. A part of patients should be considered cochlear implantation.
出处
《临床耳鼻咽喉科杂志》
CAS
CSCD
北大核心
2003年第1期12-13,共2页
Journal of Clinical Otorhinolaryngology
