摘要
目的:探讨中枢神经系统非典型畸胎样/横纹肌样瘤(AT/RT)的临床表现、病理特征及影像学特点,以提高对本病的影像诊断及鉴别诊断的能力。方法:回顾分析1例经手术后病理证实为中枢神经系统非典型畸胎样/横纹肌样瘤的临床表现、影像表现,并复习相关文献。结果:CT平扫示右额部稍高密度团块状病灶,占位效应明显,周围见结片状水肿带,骨窗显示邻近骨质无破坏;MRI显示病灶在T1WI呈低信号,T2WI及液体衰减反转恢复(FLAIR)呈稍高信号,扩散加权成像(DWI)序列呈高信号,病灶信号较均匀,呈分叶状,MRI增强示病灶欠均匀强化,部分条絮样明显强化,病灶以宽基底与大脑镰相连。结论:中枢神经系统非典型畸胎样/横纹肌样瘤罕见,临床表现变现多样化,影像表现缺乏特异性,确诊仍然需要病理组织学检查。
Objective:To explore the clinical manifestations,histopathological features,and imaging characteristics of atypical malformation/rhabdoid tumor(atypical teratoid/rhabdoid tumor)of the central nervous system,to improve the ability of imaging diagnosis and differential diagnosis of this disease.Methods:Clinical realization and imaging findings of an atypical abnormal pattern/rhabdoid were reviewed.Results:Computed tomography revealed a slightly dense right frontal lobe and the lesion had a significant occupancy effect with a visible band of nodular edema around it.The bone window showed no adjacent bone destruction.Magnetic resonance imaging(MRI)revealed the lesion as low signal on T1 and T2-weighted imaging,and fluid attenuation and inversion recovery had a slightly higher signal.A diffusion-weighted imaging(DWI)sequence showed high signal,uniform lesion signal,and lobulation.MRI enhancement showed less uniform enhancement,edge line enhancement,and a broad base attached to the brain stem.Results:Atypical teratoid/rhabdoid tumors of the central nervous system are rare,with diverse clinical manifestations,lack of specificity of imaging findings,and histopathological examination is still required for diagnosis.
作者
程少磊
王琼
王乙丞
胡兴荣
倪程
CHENG Shaolei;WANG Qiong;WANG Yicheng;HU Xingrong;NI Cheng(Hubei University of Medicine,Shiyan 442000,China;Department of Radiology,Enshi Tujia and Miao Autonomous Prefecture Central Hospital,Enshi 445000,China;Medical Science Department of Hubei University for Nationalities,Enshi 445000,China)
出处
《CT理论与应用研究(中英文)》
2025年第4期707-713,共7页
Computerized Tomography Theory and Applications
