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婴儿痉挛症研究进展 被引量:3

Research progress on infantile spasm
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摘要 婴儿痉挛症(infantile spasms)是婴儿期发病率最高的癫痫综合征,发病率为0.16/1000~0.42/1000,男女患儿比例6∶4。婴儿痉挛症幼儿期起病,起病隐匿、症状不明显,需与多种疾病相鉴别。存在孤立或成串异常动作伴或不伴发育迟滞及发育倒退时,应尽快完善脑电图及长程脑电图,并依据其脑电图尽快予患儿相应药物,改善预后。本文查阅近10年国内外相关文献,对婴儿痉挛症的病因、临床特点及影像学表现进行综述。 Infant spasm is the highest incidence of infantile epilepsy syndrome,the incidence is 0.16/1000-0.42/1000,the proportion of male and female children is 6/4.Infantile spasms starts in early childhood,and is hidden,the symptoms of infantile spasms need to be distinguished from other diseases.In the presence of isolated or series of abnormal movements with or without developmental retardation orregression,timely EEG is necessary.And according to the EEG,doctors could give the corresponding drugs to the children as soon as possible to improve the prognosis.Through the correlative literature in recent 10 years,we summarized the causes,the clinical characteristics and the iconography of isnfantile spasms.
作者 赵贺 吴琼 王华 Zhao He;Wu Qiong;Wang Hua(Department of Pediatrics,Shengjing Hospital of China Medical University,Shenyang 110004,China)
出处 《中国小儿急救医学》 CAS 2020年第3期222-224,共3页 Chinese Pediatric Emergency Medicine
基金 辽宁省博士科研启动基金计划项目(2019-BS-280)。
关键词 婴儿痉挛症 头核磁 脑电图 抗癫痫治疗 Infantile spasm Head MRI Electroencephalogram Antiepileptic therapy
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