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先天性胆总管囊性扩张症诊治进展 被引量:1

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摘要 先天性胆总管囊性扩张症(congenital cystic dilation ofthe common bile duct)俗称胆总管囊肿,1723年由Vater首次对其进行了描述,迄今文献报道近2000例.本病可发生于任何年龄,好发于婴幼儿,男女比例1:4-5,10岁以下发病者约占2/3,在西方国家其发病率低,约为1/1.3万-1.5万;但在东方国家则较高,在日本高达1/1000.本文就该病的病因、病理、临床表现以及诊断治疗作一简述.
出处 《消化外科》 CSCD 2002年第2期144-147,共4页 Journal of Digestive Surgery
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