以最后区综合征为首发表现的视神经脊髓炎谱系疾病(附2例报告及文献复习)
摘要
目的探讨视神经脊髓炎谱系疾病(NMOSD)的临床特点。方法回顾性分析2例以最后区综合征(不明原因的呃逆、恶心和呕吐)为首发症状NMOSD患者的临床表现和辅助检查特点,结合国内外文献,复习和总结NMOSD的临床特点和诊治方法。结果 2例患者均有脑干、第四脑室周围、颈髓受累。1例累及视神经。血清水通道蛋白4(AQP4)抗体均(+),予大剂量甲泼尼龙冲击治疗后症状明显改善。结论最后区综合征是NMOSD的特征性表现,早期识别最后区综合征对疾病诊断和治疗尤为重要。
出处
《中国临床神经科学》
2017年第4期440-443,共4页
Chinese Journal of Clinical Neurosciences
二级参考文献8
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共引文献7
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1龚帆,俞晓飞.温中健脾祛湿法治疗极后区综合征的临床运用[J].上海中医药杂志,2020,54(S01):17-18. 被引量：1
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