摘要小儿门静脉海绵样变（cavernous transformation of portal vein,CTPV）,是一种较罕见的小儿门静脉系统疾病,主要由于先天性或后天性因素所致门静脉主干或分支完全或部分阻塞,从而引起门静脉压力增高,机体为减轻门静脉高压在肝门区形成大量侧支循环血管丛,从而引起门静脉高压[1]。形成门静脉高压后,主要表现为门静脉高压症和继发的食管胃底静脉曲张破裂和（或）伴有门静脉高压性胃病,患者可反复呕血和柏油便,
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