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肝豆状核变性的临床表现和CT脑扫描 被引量:4

CLINICAL PICTURE AND BRAIN CT SCAN OF HEPATOLENTICULAR DEGENERATION
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摘要 对我院1984—1987年收治的17例肝豆状核变性患者的临床和脑CT扫描的相关性进行了探讨。脑CT发现双侧豆状核区低密度灶9/17例(53%),其中3例同时累及丘脑。弥漫性脑萎缩14/17例(82.4%)。临床表现和脑CT改变有一定的相关关系。硫酸锌等驱铜治疗的药物效果良好,惜无CT复查资料。 Brain CT scan of 17 patients with hepatolenticular degeneration with a clinical history ranged from 2 months to 10 years were studied from 1984 through 1987 in collaboration with their clinical manifestation. The brain CT findings were low density plaques in the lenticular nuclei on both sides in 9/17 cases ( 53% ) , 3 cases with additional involvement of thalamus, and diffuse brain atrophy in 14/17 cases (82.4%) .Clinical pictures were correlated with the brain CT scan.Zinc sulfate and other copper eliminating therapy had favorable response, but follow up CT was not available.
出处 《湖南医科大学学报》 CSCD 1989年第3期271-273,共3页 Bulletin of Hunan Medical University
关键词 肝豆状核变性 CT 脑损害 计算机 hepatolenticular degeneration brain damage, chronic tomography, X-ray, computed
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