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获得性血友病A免疫抑制剂的治疗进展 被引量:1

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摘要 获得性血友病A是一种发病率极低但病死率较高的自身免疫性疾病。多种原因导致患者体内产生了特异结合、灭活凝血因子Ⅷ的凝血因子抑制物而发病。患者在其体内凝血因子抑制物完全清除之前都处于严重出血甚至致死的风险之中。因此,如何正确合理地选择免疫抑制剂来进行抑制物清除治疗是消除患者出血风险,达到长期稳定完全缓解以及最终治愈该病的重要环节。
作者 魏卿 牛挺
出处 《华西医学》 CAS 2014年第4期646-650,共5页 West China Medical Journal
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