摘要
目的探讨儿童肝脏间叶错构瘤的临床特征、诊断与治疗。方法对10例肝脏间叶错构瘤患儿术前均行腹部B型超声、增强CT及血甲胎蛋白检查。6例行右半肝切除术,2例行肝左三叶切除术,2例行左外叶切除术。结果10例患儿均顺利完成手术,无并发症发生,术后7~9d痊愈出院。所有患儿随访6~48个月,腹部B型超声检查无肿瘤复发。复查AFP均正常,患儿生长发育良好。结论肝脏间叶错构瘤与肝脏恶性肿瘤有类似的临床症状和体征,常伴甲胎蛋白升高,临床上容易与肝脏恶性肿瘤混淆。外科手术是最佳治疗方法,可行肿瘤局部切除或规范性肝切除术,肿瘤完整切除后,偶有复发或恶变,需定期随访复查。
Objective To explore the clinical characteristics, diagnosis and treatment of hepatic mesenchymal hamartoma in children. Methods All cases were diagnosed with B-ultrasonography, computed tomography scan and alpha fetoprotein (AFP). All patients underwent operations of right hemihepatectomy (n = 6), left trilobectomy (n = 2) and left hemihepatectomy (n = 2). Results All operations were successful without complications. Discharge was within 7 9 days. During a follow-up period of 6-24 months, all patients achieved tumor-free survival with a normal level of AFP. Conclu- sions Hepatic mesenchymal hamartoma and hepatoblastoma have similar clinical characteristics. The first-choice treatment is either local tumor resection or hepatectomy. And long-term follow-ups are of- ten necessary.
出处
《中华小儿外科杂志》
CSCD
北大核心
2014年第2期97-99,共3页
Chinese Journal of Pediatric Surgery
关键词
儿童
肝脏
错构瘤
甲胎蛋白
外科手术
Child
Liver
Hamartoma
Alpha-fetoproteins
Surgical procedures,operative