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石骨症的影像学诊断 被引量:2

Analysis of Image Performance Diagnosis Osteopetrosis
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摘要 目的:探讨石骨症影像学检查方法的选择,影像表现及其诊断和鉴别诊断价值。材料与方法:对经临床证实的15例石骨症患者的临床资料和影像表现结合文献进行回顾性分析,其中男性10例,女性5例。结果:影像主要表现为骨硬化、成型异常和骨中骨。全身大部分或所有骨骼密度增高硬化占80%,但下颌骨很少累及,颅骨亦较轻。骨硬化表现为无定形、横行带状或纵行长条状。硬化区骨结构消失而不能辨认。实验室检查指标红细胞、血红蛋白、血小板减少。结论:影像检查是石骨症的主要检查方法,可显示病变的累及部位、范围和程度,对石骨症的诊断和鉴别诊断具有重要价值。 Purpose: To evaluate Image signs of the osteopetrosis.Materials and Methods: Review and analyze clinical con-firmed Image appearances and diferential diagnosis of 15 patients with osteopetrosis.Results: Osteoselerosis,abnormal shape and bone-in-bone were the main appearances in Image.The most or all bone of body were sclerosis.but the mandi-hie almost involved.It was light in cranium too.Significant difference could be found in degree and covering of osteosclerosis.The density variation conld be from slight to marked,and be related to the age of the disease beginning.Shapelessness,longitudinal and transveme strips were the manifestation of osteosclerosis.The structure of bone in sclerosis zone(compact bone,me-dullary aeavity,epiphysial cartilage and trabecular) disappeared and could not be identified.Conclusion: Image plain is the main examing method of osteopetrosis,the place,covering and degree that involved could be appeared,it has important role of the diagnosis of the osteopetrosis.
出处 《现代医用影像学》 2013年第2期102-104,共3页 Modern Medical Imageology
关键词 石骨症 影像表现 诊断 Osteoptresis Image performance manifestation Diagnesis
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