摘要
目的全面介绍先天性囊性腺瘤样畸形(CCAM)其可能的病因,临床、病理特点及诊断手段,循证探讨针对CCAM的治疗方法及预后。方法对我院2011年11月收治的1例罕见的CCAM患者的临床资料进行分析,并对相关文献进行复习。结果患者数次误诊后最终诊断为CCAM,予手术治疗后痊愈,随访1年无复发。结论 CCAM是一种少见的、非遗传性的、错构瘤样的肺发育异常,为一种良性的肺部畸形,其特点是局部肺终末呼吸性细支气管过度生长。CCAM多通过产前影像学检查、活组织检查或术后病检诊断。手术为治愈该病的最根本、最重要措施。
Objective To introduce the proposed causes, clinicopathological characteristics, management strategies and prognosis of congenital cystic adenomatoid malformation of lung （CCAM）. Methods Clinical data of a rare case of CCAM diagnosed in November 2011 in our hospital was analyzed and related literature was reviewed. Results The 66-year-old patient was finally diagnosed to have CCAM after several years of misdiagnosis and treated with surgery. After one year follow-up, his condition was stable and no recurrence happened. Conclusions CCAM is a rare developmental, non-hereditary, hamartomatous abnormality of the lung. It is considered as benign dysplastic lung tumor characterized by overgrowth of the terminal respiratory bronchioles at the expense of the saccular spaces. The CCAM is often diagnosed by prenatal imaging techniques, biopsy or postoperative pathologic results. The preferred therapy is operation.
出处
《华西医学》
CAS
2013年第4期489-493,共5页
West China Medical Journal
关键词
先天性囊性腺瘤样畸形
错构瘤
手术治疗
Congenital cystic adenomatoid malformation of lung
Hamartoma
Surgery
