摘要
目的探讨特发性门脉高压(IPH)的临床表现、诊断及治疗方法。方法结合1例特发性门脉高压患者的临床资料并进行文献复习。结果本例IPH主要表现为原因不明的门脉高压、食管胃底静脉曲张、脾功能亢进及由此引起的全血细胞减少,肝穿刺病理示肝内无明确肝硬化表现;部分性脾栓塞术后,血象5天内升至正常。结论 IPH引起的脾功能亢进,部分性脾栓塞术是治疗脾功能亢进的有效方法。
Objective To study the clinical manifestation, diagnosis, and treatment of idiopathic portal hypertension （IPH）. Methods Report a case of IPH and review the related literature. Results The case is characterized clinically by cryptogenic portal hypertension, esophageal varices, splenomegaly, and hypersplenism accompanied by pancytopenia with unknown etiology. The fiver biopsy specimen showed no obvious cirrhosis. After partial splenic embolization （PSE）, platelet and leukocytic counts increased to normal value in 5 days. ConcluMon PSE is effective for the treatment of hyDersplenism caused by IPH.
出处
《罕少疾病杂志》
2012年第5期29-32,共4页
Journal of Rare and Uncommon Diseases
关键词
特发性门脉高压
脾功能亢进
栓塞
治疗性
Idiopathic portal hypertension Hypersplenism Embolization, therapeutic
