摘要
临床无肌病性皮肌炎被认为是皮肌炎的一种少见类型,是指具有皮肌炎的典型皮损,临床上不表现为肌无力,肌酶谱正常或仅轻度异常,分为无肌病性皮肌炎和低肌病性皮肌炎。部分患者与严重的肺部病变及恶性肿瘤相关,而部分严重患者对糖皮质激素治疗不敏感,故早期发现和正确认识该病并给予合理的干预,对改善患者预后非常重要。
Clinically amyopathic dermatomyositis（C-ADM） is a rare form of dermatomyositis （DM）, in which typical skin changes contrast with minimal or absent muscle abnormalities, including amyopathic dermatomyositis （ADM） and hypomyopathic dermatomyositis （HDM）. In some cases, it is associated with severe lung lesions and malignant tumors. Patients with severe disease of this kind are unresponsive to glucocorticoids. So early detection and correct understanding of the disease, and a proper intervention to it is very important for improving patient outcomes. In this paper, the diagnosis and treatment of clinically amyopathic dermatomyositisare are summarized as follows.
出处
《实用皮肤病学杂志》
2012年第5期275-277,共3页
Journal of Practical Dermatology
关键词
皮肌炎
临床无肌病性
肺病
间质性
诊断
治疗
Dermatomyositis
Clinically amyopathic
Lung disease, interstitial
Diagnosis
Treatment
