摘要
腺泡状软组织肉瘤是一种少见的软组织恶性肿瘤,发生于腹膜后的腺泡状软组织肉瘤极为罕见,主要表现为无痛性生长的软组织肿块.国内外报道罕见,且易与副神经节瘤、腺泡状横纹肌肉瘤、肾透明细胞癌、颗粒细胞瘤混淆.本文报道腹膜后的腺泡状软组织肉瘤1例,结合影像学、临床病理学特征、免疫组织化学及基因检测技术,作出了正确诊断及治疗,并结合相关文献进行分析讨论,进一步提高了对腹膜后的腺泡状软组织肉瘤的认识.
Alveolar soft-part sarcoma is a rare type of malignant soft tissue tumor that usually presents as a painless,slow-growing mass and is easily misdiagnosed as paraganglioma,alveolar rhabdomyosarcoma,clear cell renal cell carcinoma,or granular cell tumor.Alveolar soft-part sarcoma of the retroperitoneum is extremely rare.Here we report a case of retroperitoneal alveolar soft–part sarcoma that was correctly diagnosed based on a combination of imaging,clinical and pathological features and the use of immunohistochemical and gene detection techniques.A literature review was performed to further raise the awareness of this rare disease.
出处
《世界华人消化杂志》
CAS
北大核心
2012年第22期2115-2117,共3页
World Chinese Journal of Digestology
关键词
腹膜后
腺泡状软组织肉瘤
诊断
Retroperitoneal
Alveolar soft-part sar-coma
Diagnosis
