摘要
目的 回顾总结布加综合征的临床资料 ,分析误诊原因。方法 分析总结北京协和医院 1983～ 1998年 2月收治的布加综合征 90例。结果 本组病人发病率男女之比为 1 57∶1,发病年龄 6～ 6 3岁 ,病程 15天～ 30年。临床表现前 3位分别是胸腹背壁静脉显露 (85 56 % )、肝肿大(75 56 % )和腹水 (72 2 2 % )。辅助检查方法主要是Doppler血管彩超和下腔静脉造影 ,诊断成功率分别为 97 73%和 10 0 %。 6 8例接受手术治疗 ,术式为根治术、各种类型的分流或转流术及血管内支架植入术。 56例 (6 2 2 2 % )有过误诊 ,误诊的前 2位疾病是肝硬化 (4 4 4 4 % )、结核性腹膜炎(6 6 6 % )。结论 需提高布加综合征的早期诊断率 ,积极介入治疗 ,提高患者生存率。
Objective Make a retrospective study of Budd Chiari syndrome (BCS) and analyse the causes of misdiagnosis of this disease. Methods To analyse 90 cases of BCS in PUMC hospital from 1983 to February 1998. Results Sex ratio of incidence of this group of patients is 1.57 to 1 (male to female).Age of the onset of BCS is from 6 to 63 years old and the course of BCS is from 15 days to 30 years.The first 3 clinical manifestation of BCS are uarices of chest,abdominal and dorsal wall (85.56%),hepatomegaly (75.56%) and ascites (72.22%).The main examination methods are Doppler vascular ultrasound and angiography,with 97.73% and 100% diagnostic rate.68 patients received surgical treatments which include radical,various shunting and intravascular stand embedding operation.56 patients (62.22%) had ever been mis diagnosed.The common diseases of misdiagnosis are liver cirrhosis (44.44%) and tuberculosis peritonitis (6.66%). Conclusions The early diagnostic rate of BCS should be elevated.Intervening treatment should be taken vigorously in order to enhance the living rate of BCS patients.
出处
《北京医学》
CAS
北大核心
2000年第1期10-12,共3页
Beijing Medical Journal
