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青少年肌阵挛癫痫临床研究(附30例报道) 被引量:2

Reports of Thirty cases with Juvenile Myoclonus Epilepsy Syndrome
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摘要 目的探讨青少年肌阵挛癫痫的临床特点。方法总结30例青少年肌阵挛癫痫患者的临床表现、脑电图特征和治疗预后。结果 30例青少年肌阵挛癫痫患者临床均有肌阵挛发作,合并失神发作3例、合并全面强直阵挛发作27例,其中单独以肌阵挛为表现的3例;脑电图检查均可见到暴发高幅的棘慢波;应用丙戊酸钠、左乙拉西坦无发作23例,明显减少7例。结论青少年肌阵挛癫痫是一种少见的癫痫综合征,临床过程呈良性发展。如能正确诊断,预后较好,需提高医生对该综合征的认识。 Objective The clinical manifestation,EEG and prognosis of 30 juvenile myoclonus epilepsy cases were retrospectively reviewed and improve the understanding of this syndrome.Results All 30 patients were associated with myoclonus,3 patients had no epilepsy,27 patients hadgeneralized tonic-clonic Seizure.Only three patients were associated with myoclonus butwithout other symptoms.EEG showed episodic high sharp and slow waves.Valporat or/and levetiracetam were used for the treatment.Twenty-three patients were seizure free and 7 patients improved significantly.Conclusion Juvenile myoclonus epilepsy is a rare type of Epilepsy syndrome.The outcome could be improved if diagnosed and treated appropriately.Physicians should pay more attention and understand more about this syndrome.
出处 《北京医学》 CAS 2011年第4期286-288,共3页 Beijing Medical Journal
关键词 肌阵挛 癫痫 Myoclonus Epilepsy
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参考文献11

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二级参考文献1

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