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Caroli病1例 被引量:2

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摘要 患者,男,71岁,因肺心病1年复查于2005年12月12日入院。患者30年前曾诊断为肝弥漫性病变,但无反复发热、肝区疼痛、黄疸及恶心、呕吐等病史。既往无肝炎病史及大量饮酒史,父母非近亲结婚,否认家族中遗传病史。入院查体:T36.5℃,P 88次/min,R 22次/min,BP 120/80 mmHg。神志清楚,查体合作,颜面、口唇及甲床轻度发绀。皮肤黏膜无黄染,气管居中。
出处 《疑难病杂志》 CAS 2010年第7期495-495,共1页 Chinese Journal of Difficult and Complicated Cases
关键词 CAROLI病 诊断 治疗
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参考文献3

  • 1Vachell HR, Stevens WM. Case of intrahepatic calculi [ J]. Br Med J, 1906,1 (4) :434-436.
  • 2McWhorter GL. Congenital cystic dilataion of the bild and pancreatic ducts[ J]. Arch Surg, 1939,38(4) :597411.
  • 3王鸿慧,孔瑞,孙备.Caroli’s病的研究进展[J].哈尔滨医科大学学报,2006,40(6):518-519. 被引量:14

二级参考文献20

  • 1De Tommaso AM,Santos DS,Hessel G.Caroli's disease:6 case studies[J].Acta Gastroenterol Latinoam,2003,33(1):47-51.
  • 2Abouchacra S,Toumeh S,Boobes Y,et al.An atypical course of Caroli's disease in a renal transplant patient-case report and review of the literature[J].Clin Nephrol,2004,61(4):282-288.
  • 3Madjov R,Chervenkov P,Madjova V,et al.Caroli's disease.Report of 5 cases and review of literature[J].Hepatogastroenterology,2005,52(62):606-609.
  • 4Bettini G,Mandrioli L,Morini M.Bile duct dysplasia and congenital hepatic fibrosis associated with polycystic kidney(Caroli syndrome) in a rat[J].Vet Pathol,2003,40(6):693-694.
  • 5Torra R,Badenas C,Darnell A,et al.Autosomal dominant polycystic kidney disease with anticipation and Caroli's disease associated with a PKD1 mutation.Rapid communication[J].Kidney Int,1997,52 (1):33-38.
  • 6Parada LA,Hallen M,Hagerstrand I,et al.Clonal chromosomal abnormalities in congenital bile duct dilation (Caroli's disease)[J].Gut,1999,45(5):780-782.
  • 7Sato Y,Harada K,Kizawa K,et al.Activation of the MEK5/ERK5 cascade is responsible for biliary dysgenesis in a rat model of Caroli's disease[J].Am J Pathol,2005,166(1):49-60.
  • 8Lesmana CR,Harris A,Kooshartoro A,et al.Hepatic cirrhosis caused by Caroli disease[J].Acta Med Indones,2005,37(1):33-35.
  • 9Karim AS.Caroli's disease[J].Indian Pediatr,2004,41(8):848-850.
  • 10Tamiolakis D,Arvanitidou V,Nikolaidou S,et al.Caroli's syndrome.A case report and review of the literature[J].Minerva Gastroenterol Dietol,2004,50(2):179-181.

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