摘要
目的探讨马凡氏综合征大血管病变的影像表现,评价影像对其主动脉病变及继发病变的诊断价值。方法告马凡氏综合征5例,行升主动脉瘤切除Bentall术2例,结合文献进行回顾性分析心脏大血管的MRI表现。结果马凡氏综合征心脏大血管MRI主要表现为:①主动脉窦部瘤样扩张;②左房受压;③左室扩大,室壁增厚;④主动脉瓣关闭不全及升主动脉扩张;⑤二尖瓣脱垂、二尖瓣关闭不全;⑥可合并主动脉夹层。结论 MRI在显示马凡氏综合征心脏大血管病变的部位,形态特点,继发性改变或并发症以及鉴别诊断上具有显著的优越性。
Objective To study clinical imaging features of cardiovascular anomalies in Marfan’s syndrome, and to evaluate imaging potentiality in the diagnosis of aortic pathological anomalies of the disease and the secondary changes it caused. Methods Cardiovascular features of 5 cases with Marfan’s syndrome were presented and the retrospective analysis combining with literature was done. Results MRI features of cardiovascular anomalies of the disease include： 1.aneurismal dilatation of aortic sinus; 2.compression of left atrium;3.enlargement of left ventricular and hypertrophy of its wall; 4.aortic insufficiency and dilatation of ascending aorta; 5.mitral valve prolapse, mitral insufficiency; 6.dissecting aneurysm of aorta could be complicated. Conclusion MRI has the superiority in showing the site, pathologic features, secondary changes and complication of cardiovascular system in Marfan’s syndrome as well as in making differential diagnosis of the disease.
出处
《中国CT和MRI杂志》
2010年第3期11-14,共4页
Chinese Journal of CT and MRI
关键词
马凡氏综合征
主动脉病变
磁共振成像
Marfan’s syndrome
Aortic disease
Magnetic resonance imaging
