摘要
本文分析了我院1978年11月～1997年1月儿科住院和溶血性疾病1897例1902人次，占同期儿科住院总人次37004的5．14％。1897例中，诊断明确的有1614例（85．08％）。其中最常见为红细胞G—6—PD缺陷症，占40．48％；血红蛋白病、新生儿ABO溶血病分别各占19．35％和16．55％。遗传性球形细胞增多症占1．06％，其它病因未明的溶血性贫血占11．65％。本组病例中，MN血型不合性溶血病及重型p地贫合并Rh血型不合、输血后溶血、重型p地贫合并自身免疫性溶血性贫血各1例。溶血性疾病发病以新生儿期为最高，占半数以上。加强对新生儿高胆溶血的研究尤其是对红细胞G——6——PD缺陷溶血发生的防治，有现实意义。
In this paper, 1897 cases with hemolytic diseases hospitalized in our hospital from Nov1978 to Jan 1997 were analysed. Of 1897, G-- 6--PD deficiency was 40. 98%, which was themost common hemolytic diseases in this region， hemaglobinopathies were 19. 35%, neonatalhemolytic diseases due to ABO incompatibility was 16. 55%, hereditary spherocytosis was 1.06%. There were 11. 65% cases whose etiology of hemolysis were still not clear. In thisgroup I there were 3 rare cases of Rh incompatibility: MN incompatibility (1 case), 5--tha-lassemia major with auto immunohemolytic anemia (1 case),8--thalassemia major with acutehemolysis followingtransfusion due to Rh incompatibility (1 case). Over half cases of thisgroup were newborn infants Therefore, it is important to study further on the neonatal hy-perbilirubinemia, especially on the G-- 6--PD deficiency.
出处
《中国小儿血液》
1998年第1期20-22,41,共4页
China Child Blood
