摘要
目的:探讨遗传性出血性毛细血管扩张症患者累及肺、肝脏时的CT表现。方法:应用螺旋CT扫描观察3例经临床明确诊断的遗传性出血性毛细血管扩张症患者的肺及肝脏动静脉瘘表现。结果:3例患者肺内均发现肺动静脉瘘,其中1例同时合并肝内动脉-门脉瘘。结论:增强扫描可清晰显示肺动静脉瘘影像特征-供血动脉、动脉瘤瘘及引流静脉;肝内受累表现为肝动脉、静脉及门脉迂曲扩张、肝内动脉静脉瘘,而且CT是首选的非侵袭性影像方法。
Objective： To explor the CT appearance of the lung and the liver hereditary hermorrhagic telanglectasia.Methods： cr was used to study 3 patients with hereditary hermorrhagie telangiectasia with lung and liver involvement. Results： Tuberous sclerosis frequently involved in skin, brain and kindney. On imaging, most lesions showed subendymal tuberosis, with diameters 〉 10 ram, and the water- head syndrome occurred in 1 case, the gigantocellular stellate tumor can be difinately diagnosed,in 2 cases of the group, kindney hamar- toma was found and subendymal gigantoceUular steUate tumor in 2 cases. Conclusion： CT can detect imaging characteristics of （pul- monary arteriovenous finalformation istulas） PAVMs-supplied artery, draining vein and cystic aneurysm, and the CT angingraphy of lung and liver is the first selective non-invasive imaging method for diagnosing pulmonary artefiovenous malformation and hepatic arteries were dilated and arteriovenous malformfious were found in livers.
出处
《医学影像学杂志》
2009年第11期1463-1465,共3页
Journal of Medical Imaging
