摘要
目的:总结成人心肌致密化不全(NVM)患者的临床特点。方法:回顾性分析25例 NVM 患者的临床表现、心电图、超声心动图以及心脏磁共振成像资料。结果:25例患者年龄15~75岁,其中男性18(72%)例,女性7(28%)例,其中4例有家族史。首发症状以胸闷气短最为常见共计21例,占84%,19例出现心力衰竭症状,仅1例出现脑栓塞。所有患者均伴有心律失常,类型多样。14例行心脏磁共振成像检查的患者均提示心肌致密化不全,其中6例超声心动图没有提示心肌致密化不全,其部位均累及左心。结论:NVM 发病年龄及症状差异很大,主要表现为心力衰竭和心律失常,栓塞事件少见。超声心动图是诊断 NVM的基本手段。心脏磁共振成像是诊断的重要辅助手段。
Objective:To investigate the clinic manifestation, diagnosis and treatment of non-compaction of ventricular myocardium (NVM). Methods : A total of 25 patients of non-compaction of ventricular myocardium were retrospectively analyzed. Results:The patients aged from 15 to 75 years old. 18 (72%) patients were male and 7 (28%)female. 4 patients had family history. 21 (84%) patients first suffered from the tightness of the chest and shortness of breath. Congestive heart failure happened in 19 cases. The thromboembolic event occurred in 1 patient. Various kinds of arrhythmia were observed in all patients. 14 patients underwent cardiac MRI, all of them showed NVM, and among them 6 patients meanwhile, were examined by echocardiography but NVM could not be detected,the lesions were located at the left ventricle in all 6 patients. Conclusion :The ages and symptoms vary in different patients. The most common clinical presentations of NVM were congestive heart failure and arrhythmia. Thromboembolism was rare. Echocardiography was the basic tool for examining NVM, while cardiac MRI was the more accurate method for NVM diagnosis.
出处
《中国循环杂志》
CSCD
北大核心
2008年第4期286-289,共4页
Chinese Circulation Journal
关键词
心肌致密化不伞
诊断
治疗
Non-compaction of ventricular myocardium
Diagnosis
Treatment