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成人心肌致密化不全25例临床特点分析 被引量:5

Analysis of Non-Compaction of Ventricular Myocardium in 25 Patients
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摘要 目的:总结成人心肌致密化不全(NVM)患者的临床特点。方法:回顾性分析25例 NVM 患者的临床表现、心电图、超声心动图以及心脏磁共振成像资料。结果:25例患者年龄15~75岁,其中男性18(72%)例,女性7(28%)例,其中4例有家族史。首发症状以胸闷气短最为常见共计21例,占84%,19例出现心力衰竭症状,仅1例出现脑栓塞。所有患者均伴有心律失常,类型多样。14例行心脏磁共振成像检查的患者均提示心肌致密化不全,其中6例超声心动图没有提示心肌致密化不全,其部位均累及左心。结论:NVM 发病年龄及症状差异很大,主要表现为心力衰竭和心律失常,栓塞事件少见。超声心动图是诊断 NVM的基本手段。心脏磁共振成像是诊断的重要辅助手段。 Objective:To investigate the clinic manifestation, diagnosis and treatment of non-compaction of ventricular myocardium (NVM). Methods : A total of 25 patients of non-compaction of ventricular myocardium were retrospectively analyzed. Results:The patients aged from 15 to 75 years old. 18 (72%) patients were male and 7 (28%)female. 4 patients had family history. 21 (84%) patients first suffered from the tightness of the chest and shortness of breath. Congestive heart failure happened in 19 cases. The thromboembolic event occurred in 1 patient. Various kinds of arrhythmia were observed in all patients. 14 patients underwent cardiac MRI, all of them showed NVM, and among them 6 patients meanwhile, were examined by echocardiography but NVM could not be detected,the lesions were located at the left ventricle in all 6 patients. Conclusion :The ages and symptoms vary in different patients. The most common clinical presentations of NVM were congestive heart failure and arrhythmia. Thromboembolism was rare. Echocardiography was the basic tool for examining NVM, while cardiac MRI was the more accurate method for NVM diagnosis.
出处 《中国循环杂志》 CSCD 北大核心 2008年第4期286-289,共4页 Chinese Circulation Journal
关键词 心肌致密化不伞 诊断 治疗 Non-compaction of ventricular myocardium Diagnosis Treatment
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参考文献11

  • 1Stollerger C, Finsterer J, Blazek G. Left vcntricular hypertrabeculation/ noncompaction and association with additional cardiac abnormalities and neuromuscular disorders. Am J Cardiol,2002,90 ( 8 ) : 899-902.
  • 2Chin TK, Perloff JK, William RG, ct al. Isolated noncompaction of left ventricular myocardium : A study of eight cases. Circulation, 1990,82 : 507 -513.
  • 3Jenni R, Oechslin EN,van der Loo B. Isolated ventricular non-compaction of the myocardium in adults. Heart,2007,93 ( 1 ) : 11-15.
  • 4闫朝武,赵世华,陆敏杰,蒋世良,韦云青,李世国,祁晓欧,张岩,刘玉清.左室心肌致密化不全的临床特征和磁共振成像表现[J].中华心血管病杂志,2006,34(12):1081-1084. 被引量:52
  • 5Hughes SE, McKenna WJ. New insights into the pathology of inherited cardiomyopathy. Heart, 2005,919 ( 2 ) : 257-264.
  • 6Guntheroth W, Komarniski C,Atkinson W, et al. Criterion for fetal primary spongiform cardiomyopathy: restrictive pathophysiology. Obstet Gynecol,2002,99 ( 5 Pt2 ) : 882-885.
  • 7赵亮,刘瀚旻,周同甫.双胞胎同患心肌致密化不全2例报道及文献复习[J].中华妇幼临床医学杂志(电子版),2005,1(1):69-69. 被引量:4
  • 8Weiford BC, Subbarao VD, Mulhern KM. Noncompaction of the ventricularmyocardium. Circulation ,2004,9 : 2965-2971.
  • 9矫艳,郑建伟,吴海军,晋炳申.左心室心肌致密化不全合并动脉导管未闭一例报告[J].中国医师杂志,2007,9(6):856-856. 被引量:3
  • 10Pignatelli RH, McMahon C J, Dreyer WJ, et al. Clinical characterization of left ventrieular noncompaetion in children : a relatively common form of cardiomyopathy. Circulation, 2003,108 (21) : 2672- 2678.

二级参考文献19

  • 1赵世华,陆敏杰,张岩,蒋世良,黄连军,王红宇,吴言伶,杜茉佳,刘玉清.1.5 T高端MR在心血管病诊断中的应用[J].中华放射学杂志,2005,39(6):577-581. 被引量:30
  • 2苗翠莲,张兆琪,郭曦,王珏,宴子旭,赵轶柯.孤立性心肌致密化不全的MRI诊断[J].中华放射学杂志,2005,39(6):588-592. 被引量:19
  • 3闫朝武,赵世华,陆敏杰,蒋世良,韦云青,李世国,祁晓欧,张岩,刘玉清.左室心肌致密化不全的临床特征和磁共振成像表现[J].中华心血管病杂志,2006,34(12):1081-1084. 被引量:52
  • 4Richardson P,McKenna W,Bristow M,et al.Report of the 1995 World Health Organization/International Society and Federation of Cardiology Task Force on the Definition and Classification of cardiomyopathies.Circulation,1996,93:841-842.
  • 5Engberding R,Bender F.Identification of a rare congenital anomaly of the myocardium by two-dimensional echocardiography:persistence of isolated myocardial sinusoids.Am J Cardiol,1984,53:1733-1734.
  • 6Oechslin EN,Attenhofer Jost CH,Rojas JR,et al.Long-term follow-up of 34 adults with isolated left ventricular noncompaction:a distinct cardiomyopathy with poor prognosis.J Am Coll Cardiol,2000,36:493-500.
  • 7Ritter M,Oechslin E,Sutsch G,et al.Isolated noncompaction of the myocardium in adults.Mayo Clin Proc,1997,72:26-31.
  • 8Chin TK,Perloff JK,Williams RG,et al.Isolated noncompaction of left ventricular myocardium.A study of eight cases.Circulation,1990,82:507-513.
  • 9Jenni R,Oechslin E,Schneider J,et al.Echocardiographic and pathoanatomical characteristics of isolated left ventricular non-compaction:a step towards classification as a distinct cardiomyopathy.Heart,2001,86:666-671.
  • 10Agmon Y,Connolly HM,Olson LJ,et al.Noncompaction of the ventricular myocardium.J Am Soc Echocardiogr,1999,12:859-863.

共引文献56

同被引文献54

  • 1廖玉华,袁璟.关注心肌致密化不全的临床诊断[J].临床心血管病杂志,2006,22(7):388-389. 被引量:17
  • 2闫朝武,赵世华,陆敏杰,蒋世良,韦云青,李世国,祁晓欧,张岩,刘玉清.左室心肌致密化不全的临床特征和磁共振成像表现[J].中华心血管病杂志,2006,34(12):1081-1084. 被引量:52
  • 3侯翠红,楚建民,浦介麟,吕凤英,刘蕾,赵世华,王浩,华伟,张澍.心肌致密化不全患者的临床特点及预后[J].中国循环杂志,2007,22(2):114-117. 被引量:12
  • 4李飞,朱永胜,刘兵,李虎,何光彬,李兰荪,王海昌,郭文怡.心肌致密化不全16例临床分析及随访报告[J].中国实用内科杂志,2007,27(13):1034-1036. 被引量:8
  • 5Jenni R,Oechslin EN,van der Loo B.Isolated ventricularnon-compaction of the myocardium in adults[J].Heart,2007,93(1):11-15.
  • 6Weiford BC,Subbarao VD,Mulhern KM.Noncompactionof the ventricular myocardium[J].Circulation,2004,109(24):2965-2971.
  • 7Jenni R, Oechslin E, van der Loo B. Isolated ventricular noncom- paction of the myocardium in adults[J]. Heart, 2007, 93 (1): 11- 15.
  • 8Maron B J, Towbin JA, Thiene G, et al. Contemporary definitions and classification of the cardiomyopathies." an American Heart Association Scientific Statement from the Council on Clinical C- ardiology, Heart Failure and Transplantation Committee; Qual- ity of Care and Outcomes Research and Functional Genomics a- nd Translational Biology Interdisciplinary Working Groups; and Council on Epidemiology and Prevention[J]. Circulation, 2006, 113(14): 1807-1816.
  • 9Ichida F, Tsubata S, Bowles KR, et al. Novel gene mutation in p- atients with left ventricular noncompaction or Barth syndrome [J]. Circulation, 2001,103(9): 1256-1263.
  • 10Calvillo P, Marti-Bonmati L Chaustre F, et al. MRI quantificat- ion of myocardial function, perfusion, and enhancement in pati- ents with left-ventricular noncompaction[J]. Radiologia, 2009, 51(1): 45-56.

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