非典型溶血性尿毒症综合征发病机制的研究进展
Progress in Pathogencsis of Atypical Hemolytic Uremic Syndrome
摘要
非典型溶血性尿毒症综合征（HUS）是除外志贺样毒素所致的HUS，目前尚缺乏有效的治疗手段，预后恶劣。近年的研究发现，补体旁路途径自我调节的三个重要的因子一补体H因子、膜辅蛋白和补体I因子的缺乏或功能不足与非典型HUS的发病有重要关系，深入研究它们的功能将为非典型HUS的诊断和治疗提供新的途径。
出处
《国际儿科学杂志》
2007年第3期175-177,共3页
International Journal of Pediatrics
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