摘要
目的:回顾性分析肺淋巴管肌瘤病的HRCT表现,讨论其诊断和鉴别诊断。方法:总结6例经病理证实的肺淋巴管肌瘤病,4例行支气管镜肺活检,2例经胸腔镜活检确诊。所有病例均行胸部常规CT及HRCT扫描。结果:常规胸部CT扫描见两肺密度减低,偶见囊状影,相应水平HRCT可清晰显示全肺囊状影,无分布差异。随病程进展,囊状影数目增多,部分融合成肺大泡或气胸,也可见乳糜胸水。结论:HRCT对该病的早期诊断、鉴别诊断具有重要价值,同时也是判断病变进展及预后的有效指标。
Objective：To retrospectively study the HRCT features of pulmonary lymphangiomyomatosis （PLAM） and discuss its diagnosis and differential diagnosis. Methods： HRCT scans and radiographs were obtained from 6 cases of pathologically proven patients of PLAM. Transbronchial fiberscopic lung biopsy was performed in 4 cases and thoracoscopic biopsy in other 2 cases. Routine thoracic CT and HRCT scans were both performed in all 6 cases. Results： On routine thoracic CT, reduction of radiolucencies of both lungs with several cystic loci were shown, while on the corresponding levels of the HRCT scans,cystic lesions with clear contours were found throughout the whole fields of both lungs. No difference in lesion distribution was seen. The numbers of air-filled and cystic lesions were increasing as progress of the disease occurred. Some of the air-filled cystic loci coalescing to form pneumatoceles or causing pneumothorax and chylothorax were also seen. Conclusion：HRCT is a valuable imaging modality in the early diagnosis and differential diagnosis of PLAM,furthermore,it provides effective imaging evidences for the evaluation of the progress and prognosis of the disease as well.
出处
《放射学实践》
2006年第11期1137-1139,共3页
Radiologic Practice
