摘要
本文报道一例原发性纤毛运动障碍患者的超微结构表现。该例病人具有典型的Ｋａｒｔａｇｅｎｅｒ氏综合征的临床表现。电镜观察到支气管粘膜上皮纤毛弯曲倒伏，部分相互融合，发育不良，可呈连体状，质膜有丝状突起，有的纤毛呈正方形或多角形，中央及周围微管缺失、移位和增加，内、外动力臂缺失。本文对该病的超微病理学进行了讨论。
A case of primary ciliary dyskinesia was reported.Clinically the patient exhibited the typical features ofKartagener’s syndrome. By electron microscopy the cilia of bronchial epithelial cells were found winding and in-verting,mixed together occasionally.Some cilia appeared as aplasia.There were finger-like projections in thecytoplasm with the square and polygon appearance.Displacement of the central pair of microtubles and periph-eral outer doublets,abnormalities of microtubular arrangement and defect of outer or inner dynein arms could beobserved.
出处
《电子显微学报》
CAS
CSCD
1995年第1期36-38,共3页
Journal of Chinese Electron Microscopy Society
