Comments Ebstein's Anomaly(EA)is a rare congenital heart disease(CHD)with an incidence of approximately 1 in 20,000.The pathognomonic feature involves apical displacement of the septal and posterior leaflets,resul...Comments Ebstein's Anomaly(EA)is a rare congenital heart disease(CHD)with an incidence of approximately 1 in 20,000.The pathognomonic feature involves apical displacement of the septal and posterior leaflets,resulting in valvular insufficiency and right ventricular(RV)remodeling.Untreated patients exhibit a cumulative mortality rate of up to 25% within the first decade,with heart failure(HF)and arrhythmias constituting the predominant causes of death.Current guidelines suggest that asymptomatic patients with accessory pathways may benefit from prophylactic ablation,though robust evidence specific to EA remains limited[1-3].展开更多
基金funded by E Fund Congenital Heart Disease Medical Talent Cultivation and Education Fund,grant number 2023QT0009the Science and Technology Planning Project of Guangdong Province,grant number 2023B03J1255.
文摘Comments Ebstein's Anomaly(EA)is a rare congenital heart disease(CHD)with an incidence of approximately 1 in 20,000.The pathognomonic feature involves apical displacement of the septal and posterior leaflets,resulting in valvular insufficiency and right ventricular(RV)remodeling.Untreated patients exhibit a cumulative mortality rate of up to 25% within the first decade,with heart failure(HF)and arrhythmias constituting the predominant causes of death.Current guidelines suggest that asymptomatic patients with accessory pathways may benefit from prophylactic ablation,though robust evidence specific to EA remains limited[1-3].
