遗传性Sebastian综合征（hereditary Sebastian syndrome．SBS）是一种遗传性出血性疾病，临床较为少见，易误诊为特发性血小板减少性紫癜（ITP）。为了便于临床医师更好地认识该病，我们报道1例SBS患者以及对其家系调查．并复习相关文...遗传性Sebastian综合征（hereditary Sebastian syndrome．SBS）是一种遗传性出血性疾病，临床较为少见，易误诊为特发性血小板减少性紫癜（ITP）。为了便于临床医师更好地认识该病，我们报道1例SBS患者以及对其家系调查．并复习相关文献如下。展开更多
Vladimir Vladimirovich Nabokov （1899-1977）, a Russian-born Ameri- can writer, is one of the most gifted exilic writers of the twentieth century. His first English novel, The Real Life of Sebastian Knight, which inhe...Vladimir Vladimirovich Nabokov （1899-1977）, a Russian-born Ameri- can writer, is one of the most gifted exilic writers of the twentieth century. His first English novel, The Real Life of Sebastian Knight, which inherits certain aesthetic motifs of his Russian works, such as the artist in exile, the motif of the double, and the theme of the other world, has attracted the academic circle and received extreme views spreading between the good and the bad. But the core question in the whole of Nabokov scholarship is the ambiguous identities of the novel＇s two heroes, Sebastian and V. who are half-brothers. It is the identity puzzle that makes this novel more and more popular in Nabokov criticism. This essay attempts to review past reviews concerning this problem and analyze the four interpretations occa- sioned by the identity puzzle in Nabokov criticism.展开更多
The aim of this essay is to consider how Tieck uses the Narrheit concept in his work Der gestiefelte Kater as a key to interpretation.In doing so,it is also possible to grasp the semantic variability and the multiple ...The aim of this essay is to consider how Tieck uses the Narrheit concept in his work Der gestiefelte Kater as a key to interpretation.In doing so,it is also possible to grasp the semantic variability and the multiple layering of the Narr concept.Tieck calls some of the heroes of his comedy Narr,and through these Narren-figures intended to describe some weak points of the society of his time-he intends to reflect on the correctness of the order in late eighteenth-century society.展开更多
非肌球蛋白重链9相关疾病（nonmuscle myosin heavy chain 9 related diseases,MYH9-RD）是一种少见的人类常染色体显性遗传性血液疾病,具有典型的巨大血小板、血小板减少和粒细胞包涵体三大特点以及肾脏受累、听力受损和白内障等临床表...非肌球蛋白重链9相关疾病（nonmuscle myosin heavy chain 9 related diseases,MYH9-RD）是一种少见的人类常染色体显性遗传性血液疾病,具有典型的巨大血小板、血小板减少和粒细胞包涵体三大特点以及肾脏受累、听力受损和白内障等临床表型.由于此病临床表型不一,具体可以分为May-Hegglin异常、Epstein综合征、Fechtner综合征、Sebastian综合征[1].2003年,Seri等[2]研究认为,以上4种疾病都是由MYH9基因突变产生的.本研究发现1例MYH9-RD散在病例.展开更多
文摘Vladimir Vladimirovich Nabokov （1899-1977）, a Russian-born Ameri- can writer, is one of the most gifted exilic writers of the twentieth century. His first English novel, The Real Life of Sebastian Knight, which inherits certain aesthetic motifs of his Russian works, such as the artist in exile, the motif of the double, and the theme of the other world, has attracted the academic circle and received extreme views spreading between the good and the bad. But the core question in the whole of Nabokov scholarship is the ambiguous identities of the novel＇s two heroes, Sebastian and V. who are half-brothers. It is the identity puzzle that makes this novel more and more popular in Nabokov criticism. This essay attempts to review past reviews concerning this problem and analyze the four interpretations occa- sioned by the identity puzzle in Nabokov criticism.
文摘The aim of this essay is to consider how Tieck uses the Narrheit concept in his work Der gestiefelte Kater as a key to interpretation.In doing so,it is also possible to grasp the semantic variability and the multiple layering of the Narr concept.Tieck calls some of the heroes of his comedy Narr,and through these Narren-figures intended to describe some weak points of the society of his time-he intends to reflect on the correctness of the order in late eighteenth-century society.
文摘非肌球蛋白重链9相关疾病（nonmuscle myosin heavy chain 9 related diseases,MYH9-RD）是一种少见的人类常染色体显性遗传性血液疾病,具有典型的巨大血小板、血小板减少和粒细胞包涵体三大特点以及肾脏受累、听力受损和白内障等临床表型.由于此病临床表型不一,具体可以分为May-Hegglin异常、Epstein综合征、Fechtner综合征、Sebastian综合征[1].2003年,Seri等[2]研究认为,以上4种疾病都是由MYH9基因突变产生的.本研究发现1例MYH9-RD散在病例.
