“新威洋”轮第36航次,空载(船舶吃水7.40m/11.40m),接到明确的航次指令后,驶往巴西ANGRA DOS REIS港办理进港手续。港口锚地相关情况ANGRA DOS REIS港是巴西东南部里约热内卢州的一个重要港口,位于大西洋沿岸,里约热内卢西南约80海里,...“新威洋”轮第36航次,空载(船舶吃水7.40m/11.40m),接到明确的航次指令后,驶往巴西ANGRA DOS REIS港办理进港手续。港口锚地相关情况ANGRA DOS REIS港是巴西东南部里约热内卢州的一个重要港口,位于大西洋沿岸,里约热内卢西南约80海里,是巴西能源产业的重要支点。展开更多
为了提高传统全网遍历限流方案的求解效率,面对大规模电力系统,给出一种基于改进REI等值法的网架调整限流策略。将网络等值技术与500 k V网架调整限流机理相结合,根据支路限流灵敏度指标对原系统进行一次预处理,将其划分为研究系统和若...为了提高传统全网遍历限流方案的求解效率,面对大规模电力系统,给出一种基于改进REI等值法的网架调整限流策略。将网络等值技术与500 k V网架调整限流机理相结合,根据支路限流灵敏度指标对原系统进行一次预处理,将其划分为研究系统和若干外部子系统。再利用改进的动态REI等值法对各子系统进行化简,以等值过程中各发电机在虚拟支路上的功率传输因子来确定等值发电机的参数。通过在两个算例上的仿真验证,结果表明改进后的REI等值法能够较好地保留原系统的动态特性,同时迅速筛选出最优限流开断线路方案。展开更多
AIM: To analyze mutations in transforming growth factor beta-induced (TGFBI) gene in a Chinese pedigree with Reis-Bücklers corneal dystrophy (RBCD,also known as GCD3).METHODS: In a five-generation Chinese family,...AIM: To analyze mutations in transforming growth factor beta-induced (TGFBI) gene in a Chinese pedigree with Reis-Bücklers corneal dystrophy (RBCD,also known as GCD3).METHODS: In a five-generation Chinese family,eight members were identified with RBCD and the rest were unaffected.All members of the family underwent complete ophthalmologic examinations.Exons of TGFBI were amplified by polymerase chain reaction,sequenced,and compared with a reference database.RESULTS: A single heterozygous C>T (R124C) point mutation was found in exon 4 of TGFBI in all the affected members of the pedigree,but not in the unaffected members.CONCLUSION: R124C which was a known mutation for lattice corneal dystrophy type I,segregated with the RBCD in this pedigree.This elucidated the correlation between genotype and phenotype in a Chinese family of RBCD.展开更多
基金Project Supported by National Natural Science Foundation of China(NSFC)(50777021)Project Supported by Guangdong Key Laboratory ofClean Energy(2008A060301002)~~
文摘为了提高传统全网遍历限流方案的求解效率,面对大规模电力系统,给出一种基于改进REI等值法的网架调整限流策略。将网络等值技术与500 k V网架调整限流机理相结合,根据支路限流灵敏度指标对原系统进行一次预处理,将其划分为研究系统和若干外部子系统。再利用改进的动态REI等值法对各子系统进行化简,以等值过程中各发电机在虚拟支路上的功率传输因子来确定等值发电机的参数。通过在两个算例上的仿真验证,结果表明改进后的REI等值法能够较好地保留原系统的动态特性,同时迅速筛选出最优限流开断线路方案。
基金Supported by grants from the National Natural Science Foundation of China (No. NNSF 81000370)
文摘AIM: To analyze mutations in transforming growth factor beta-induced (TGFBI) gene in a Chinese pedigree with Reis-Bücklers corneal dystrophy (RBCD,also known as GCD3).METHODS: In a five-generation Chinese family,eight members were identified with RBCD and the rest were unaffected.All members of the family underwent complete ophthalmologic examinations.Exons of TGFBI were amplified by polymerase chain reaction,sequenced,and compared with a reference database.RESULTS: A single heterozygous C>T (R124C) point mutation was found in exon 4 of TGFBI in all the affected members of the pedigree,but not in the unaffected members.CONCLUSION: R124C which was a known mutation for lattice corneal dystrophy type I,segregated with the RBCD in this pedigree.This elucidated the correlation between genotype and phenotype in a Chinese family of RBCD.
