A 40-year-old man with haemopbysis and serious spontaneous hemothorax. Chest computed tomography showed multiple flakes in his lungs, nodules shadow, right pleural effusion with right pulmonary atelectasis The patholo...A 40-year-old man with haemopbysis and serious spontaneous hemothorax. Chest computed tomography showed multiple flakes in his lungs, nodules shadow, right pleural effusion with right pulmonary atelectasis The pathological specimens obtained by thoracic surgery revealed pulmonary angiosarcoma. Primary pulmonary angiosarcoma is a rare malignant tumor and is lack of typical clinical symptoms and imaging features, diagnosis mainly depend on histopathologic features and immunohistochemical analysis. There is no effective therapy for pulmonary vascular sarcoma. Integrated treatment can may extend the survival time of patients.展开更多
Primary pulmonary angiosarcoma is rare,accounting for about 2%of all lung tumors.Male incidence is five times highe-r than female.The clinical symptoms and imaging findings of pulmonary angiosarcoma are nonspecific an...Primary pulmonary angiosarcoma is rare,accounting for about 2%of all lung tumors.Male incidence is five times highe-r than female.The clinical symptoms and imaging findings of pulmonary angiosarcoma are nonspecific and can be diag nosed by immunohistochemistry.The treatment of pulmonary angiosarcoma has not yet been defined,including surgery,chemotherapy,radiotherapy,poor prognosis,high mortality,most patients died within a few months after symptoms.Ste roids,cyclophosphamide,gemcitabine and paclitaxel have been reported to be used in maintenance chemotherapy.The p atient survived for one year and then died.A case of primary pulmonary angiosarcoma were treated with keytruda,and t he literature was reviewed.展开更多
文摘A 40-year-old man with haemopbysis and serious spontaneous hemothorax. Chest computed tomography showed multiple flakes in his lungs, nodules shadow, right pleural effusion with right pulmonary atelectasis The pathological specimens obtained by thoracic surgery revealed pulmonary angiosarcoma. Primary pulmonary angiosarcoma is a rare malignant tumor and is lack of typical clinical symptoms and imaging features, diagnosis mainly depend on histopathologic features and immunohistochemical analysis. There is no effective therapy for pulmonary vascular sarcoma. Integrated treatment can may extend the survival time of patients.
文摘Primary pulmonary angiosarcoma is rare,accounting for about 2%of all lung tumors.Male incidence is five times highe-r than female.The clinical symptoms and imaging findings of pulmonary angiosarcoma are nonspecific and can be diag nosed by immunohistochemistry.The treatment of pulmonary angiosarcoma has not yet been defined,including surgery,chemotherapy,radiotherapy,poor prognosis,high mortality,most patients died within a few months after symptoms.Ste roids,cyclophosphamide,gemcitabine and paclitaxel have been reported to be used in maintenance chemotherapy.The p atient survived for one year and then died.A case of primary pulmonary angiosarcoma were treated with keytruda,and t he literature was reviewed.